Morphoea en coup de sabre - DermNet
Morphoea en coup de sabre is a variant of linear morphoea (a localised form of scleroderma) restricted to the frontoparietal region (forehead). The name ‘en coup de sabre’ (the blow of a sword) derives from the characteristic scar that indents the …
Linear scleroderma “en coup de sabre” with extensive brain …
Linear scleroderma “en coup de sabre” (LSES) variant is a cephalic subtype of localized scleroderma that can be associated with extracutaneous stigmata, such as epilepsy, dementia syndromes, as well as focal central nervous system neurologic ...
Linear scleroderma | Radiology Reference Article - Radiopaedia.org
2024年10月22日 · Linear scleroderma, also known as scleroderma en coup de sabre, is a very focal form of scleroderma classically characterized by a linear band of atrophy involving the frontal or frontoparietal scalp and subjacent thinned calvaria …
Scleroderma en coup de sabre - UpToDate
In addition, patients with en coup de sabre can have scleroderma lesions elsewhere. Neuroimaging abnormalities are common in patients with linear scleroderma of the face, although they are not … Pathogenesis, clinical manifestations, and diagnosis of morphea (localized scleroderma) in adults
En coup de sabre - PubMed
En coup de sabre (ECDS) is a rare form of localized scleroderma that typically manifests in children and women. It presents as a fibrous pansclerotic plaque extending in a bandlike distribution on the frontoparietal scalp with surrounding scarring alopecia.
Adult-onset en coup de sabre scleroderma in a patient with linear ...
The en coup de sabre variant of linear scleroderma typically occurs in children. We report a unique case of adult-onset en coup de sabre scleroderma in a patient with linear localized scleroderma profunda. The patient was treated with oral steroids and oral methotrexate improving her cutaneous disease.
Therapeutic and Reconstructive Management Options in …
2021年9月29日 · Scleroderma (morphea) en coup de sabre is a localized subtype restricted to the frontoparietal region of the head. Current treatment paradigms rely on low levels of evidence, primarily case reports and case series-supported by expert opinions.
Management Options for Linear Scleroderma ("En Coup de Sabre")
2022年10月1日 · Background: En coup de sabre (ECDS) is a form of linear-scleroderma, primarily affecting the face. Despite effectiveness of pharmacological interventions in the management of lesions, sequelae of cutaneous deformities are common.
Stroke-mimic y esclerodermia en «coup de sabre»: reporte de …
2021年10月1日 · La esclerodermia en «coup de sabre» es un tipo de EL en forma de surco que afecta al área frontoparietal, como una banda esclerótica con atrofia y adelgazamiento de las capas externas de la piel.
Esclerodermia localizada en Coup de Sabre: A propósito de un caso
2023年4月11日 · Un tipo de morfea lineal es la morfea “En Coup de Sabre” que consiste en la contracción y rigidez de la piel que culmina con una depresión de parte de la mitad del rostro, que puede...